Skin & Rashes

My Baby Has a Vascular Malformation (Port-Wine Stain or Deeper)

Medically reviewed by Dr. Sarah Chen, MD, FAAP · Board-Certified Pediatrician

Content reviewed against published ISSVA, Boston Children's, NIH guidelines

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Baby skin is sensitive and changes frequently. If you are noticing has a vascular malformation (port-wine stain or deeper), here is what you need to know.

The short answer

Vascular malformations are structural abnormalities of blood vessels or lymph vessels that are present at birth (though some become apparent later). Unlike hemangiomas, which grow rapidly and then shrink, vascular malformations grow proportionally with the child and do not go away on their own. They are classified by the type of vessel involved: capillary (port-wine stains), venous, lymphatic, or arteriovenous. Most are benign and manageable, but the approach depends on the type, location, and whether associated conditions are present (such as Sturge-Weber syndrome with facial port-wine stains).

Key takeaways

  • Vascular malformations are structural abnormalities of blood vessels or lymph vessels that are present at birth (though some become apparent later). Unlike hemangiomas, which grow rapidly and then shrink, vascular malformations grow proportionally with the child and do not go away on their own. They are classified by the type of vessel involved: capillary (port-wine stains), venous, lymphatic, or arteriovenous. Most are benign and manageable, but the approach depends on the type, location, and whether associated conditions are present (such as Sturge-Weber syndrome with facial port-wine stains).
  • Usually normal when: Your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist
  • Call your doctor if: A vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care
  • Varies by age — see the age-by-age breakdown below
Eczema is very common in babies and children. About 1 in 10 children will develop eczema, typically starting in the first few months of life.
Eczema in Babies and Children, American Academy of Pediatrics (AAP)

Parents everywhere have the same worry. You are doing the right thing by looking into it.

What Parents Should Know

According to ISSVA, Boston Children's, NIH guidelines, vascular malformations are structural abnormalities of blood vessels or lymph vessels that are present at birth (though some become apparent later). Unlike hemangiomas, which grow rapidly and then shrink, vascular malformations grow proportionally with the child and do not go away on their own. They are classified by the type of vessel involved: capillary (port-wine stains), venous, lymphatic, or arteriovenous. Most are benign and manageable, but the approach depends on the type, location, and whether associated conditions are present (such as Sturge-Weber syndrome with facial port-wine stains). At 0-6 months, vascular malformations are present at birth, though some are more obvious than others. A port-wine stain appears as a flat, pink to reddish-purple patch that does not blanch easily. Venous or lymphatic malformations may appear as soft, compressible masses or swelling. Your pediatrician may refer you to a vascular anomalies specialist. If a port-wine stain involves the forehead or upper eyelid, screening for Sturge-Weber syndrome (involving the brain and eyes) is recommended. It is generally considered normal when your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist. However, you should contact your pediatrician promptly if a vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care.

Sources: [1], [2], [3]

Normal vs. Concerning

Usually Normal
Worth Discussing
Your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist
A vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care
Your baby's vascular malformation is stable and not causing functional problems
A lymphatic or venous malformation becomes suddenly swollen, red, and painful — this may indicate infection (cellulitis) and needs immediate medical treatment
Laser treatments are lightening a port-wine stain gradually over multiple sessions
Your baby has a facial port-wine stain and develops seizures — this could indicate Sturge-Weber syndrome and requires urgent neurologic evaluation

By Age

What to expect by age

0-6 months

Vascular malformations are present at birth, though some are more obvious than others. A port-wine stain appears as a flat, pink to reddish-purple patch that does not blanch easily. Venous or lymphatic malformations may appear as soft, compressible masses or swelling. Your pediatrician may refer you to a vascular anomalies specialist. If a port-wine stain involves the forehead or upper eyelid, screening for Sturge-Weber syndrome (involving the brain and eyes) is recommended.

6-12 months

For capillary malformations (port-wine stains), pulsed dye laser (PDL) treatment can begin in infancy and is more effective when started early. Multiple sessions are needed. The goal is to lighten the stain, though complete clearance is uncommon. For lymphatic malformations, treatment depends on size and location — options include sclerotherapy (injection treatment) and surgical reduction. Your vascular anomalies team will develop a plan tailored to your baby.

1-5 years

Vascular malformations grow proportionally with the child. Port-wine stains may gradually deepen in color and develop a more pebbled texture over years if untreated. Ongoing laser treatments help maintain lighter color. Venous malformations may cause pain, particularly during physical activity or when the affected area is dependent (hanging down). Compression garments can help. Lymphatic malformations may fluctuate in size, especially during infections.

5 years+

Long-term management of vascular malformations is a marathon, not a sprint. Most are managed rather than cured. Regular follow-up with a vascular anomalies team is important. New treatments continue to emerge, including targeted medications (such as sirolimus for complex lymphatic and venous malformations). Emotional support for children living with visible vascular malformations is an important part of care.

What to Tell Your Pediatrician

  • Describe when you first noticed has a vascular malformation (port-wine stain or deeper) and how it has changed over time.
  • Note your baby's current age and which age-specific patterns you are seeing.
  • Mention if a port-wine stain on the face involves the forehead or eyelid area and has not been evaluated for Sturge-Weber syndrome.
  • Mention if a venous or lymphatic malformation seems to be growing disproportionately or causing pain.
  • Let your doctor know if you have noticed any related concerns, such as changes in feeding, sleep, or movement patterns.
  • Bring a list of any questions or observations you want to discuss at the appointment.

What Should You Do?

When to take action

Probably normal when...
  • Your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist
  • Your baby's vascular malformation is stable and not causing functional problems
  • Laser treatments are lightening a port-wine stain gradually over multiple sessions
Mention at your next visit when...
  • A port-wine stain on the face involves the forehead or eyelid area and has not been evaluated for Sturge-Weber syndrome
  • A venous or lymphatic malformation seems to be growing disproportionately or causing pain
  • The malformation is affecting function (vision, breathing, swallowing, limb movement)
  • You want to discuss treatment options or are concerned about the cosmetic impact
Act now when...
  • A vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care
  • A lymphatic or venous malformation becomes suddenly swollen, red, and painful — this may indicate infection (cellulitis) and needs immediate medical treatment
  • Your baby has a facial port-wine stain and develops seizures — this could indicate Sturge-Weber syndrome and requires urgent neurologic evaluation
  • A vascular malformation near the airway is causing difficulty breathing — call 911

What You Can Do at Home

  • Keep track of when you notice has a vascular malformation (port-wine stain or deeper) — noting the time of day, duration, and any triggers can help your pediatrician.
  • Remember that your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist — this is generally within the range of normal.
  • At 0-6 months, focus on observation rather than intervention unless your pediatrician advises otherwise.
  • Use fragrance-free, hypoallergenic products on your baby's skin. Avoid over-bathing — 2-3 baths per week is usually sufficient.
  • While monitoring at home, seek immediate care if a vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care.

My Baby's Vascular Tumor Is Causing Blood Clotting Problems (Kasabach-Merritt)

Kasabach-Merritt phenomenon (KMP) is a rare but serious complication where certain vascular tumors (kaposiform hemangioendothelioma or tufted angioma — not common infantile hemangiomas) trap platelets and clotting factors, leading to dangerously low platelet counts and a bleeding disorder. KMP is a medical emergency that requires hospitalization and specialized treatment. Despite being frightening, modern treatment with sirolimus and other medications has significantly improved outcomes. Most children respond well to treatment, though the vascular tumor may not fully resolve.

My Baby Has a Waxy Yellowish Patch on Their Scalp (Nevus Sebaceous)

A nevus sebaceous (also called nevus sebaceous of Jadassohn) is a benign birthmark that typically appears on the scalp as a flat or slightly raised, yellowish-orange, waxy or velvety patch where hair does not grow. It is present at birth and occurs in about 0.3% of newborns. During childhood, it remains relatively flat and inconspicuous. At puberty, it becomes thicker and more noticeable due to hormonal stimulation. There is a small risk (historically overstated) of developing benign or rarely malignant tumors within the nevus later in life, so monitoring and potential removal are discussed with your dermatologist.

My Baby Has a Streaky or Velvety Raised Birthmark (Epidermal Nevus)

An epidermal nevus is a benign (non-cancerous) overgrowth of skin cells that is present at birth or appears in early childhood. It typically looks like a slightly raised, skin-colored to brownish, velvety or wart-like patch that often follows a linear or streaky pattern along the body's natural skin lines (Blaschko lines). Epidermal nevi are usually isolated and purely cosmetic. However, when they are large or extensive, they can sometimes be associated with abnormalities in other organ systems (epidermal nevus syndrome), so a thorough evaluation is recommended for larger lesions.

Frequently asked questions

Is has a vascular malformation (port-wine stain or deeper) normal?
Vascular malformations are structural abnormalities of blood vessels or lymph vessels that are present at birth (though some become apparent later). Unlike hemangiomas, which grow rapidly and then shrink, vascular malformations grow proportionally with the child and do not go away on their own. They are classified by the type of vessel involved: capillary (port-wine stains), venous, lymphatic, or arteriovenous. Most are benign and manageable, but the approach depends on the type, location, and whether associated conditions are present (such as Sturge-Weber syndrome with facial port-wine stains).
When should I call the doctor about has a vascular malformation (port-wine stain or deeper)?
A vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care A lymphatic or venous malformation becomes suddenly swollen, red, and painful — this may indicate infection (cellulitis) and needs immediate medical treatment Your baby has a facial port-wine stain and develops seizures — this could indicate Sturge-Weber syndrome and requires urgent neurologic evaluation
When is has a vascular malformation (port-wine stain or deeper) normal?
Your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist Your baby's vascular malformation is stable and not causing functional problems Laser treatments are lightening a port-wine stain gradually over multiple sessions
What causes has a vascular malformation (port-wine stain or deeper)?
Vascular malformations are structural abnormalities of blood vessels or lymph vessels that are present at birth (though some become apparent later). Unlike hemangiomas, which grow rapidly and then shrink, vascular malformations grow proportionally with the child and do not go away on their own. They are classified by the type of vessel involved: capillary (port-wine stains), venous, lymphatic, or arteriovenous. Most are benign and manageable, but the approach depends on the type, location, and whether associated conditions are present (such as Sturge-Weber syndrome with facial port-wine stains). Common explanations include: Your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist. Your baby's vascular malformation is stable and not causing functional problems.
What should I mention to my pediatrician about has a vascular malformation (port-wine stain or deeper)?
You should mention has a vascular malformation (port-wine stain or deeper) at your next visit if: A port-wine stain on the face involves the forehead or eyelid area and has not been evaluated for Sturge-Weber syndrome. A venous or lymphatic malformation seems to be growing disproportionately or causing pain. The malformation is affecting function (vision, breathing, swallowing, limb movement).
Is has a vascular malformation (port-wine stain or deeper) normal at 0-6 months?
Vascular malformations are present at birth, though some are more obvious than others. A port-wine stain appears as a flat, pink to reddish-purple patch that does not blanch easily. Venous or lymphatic malformations may appear as soft, compressible masses or swelling. Your pediatrician may refer you to a vascular anomalies specialist. If a port-wine stain involves the forehead or upper eyelid, screening for Sturge-Weber syndrome (involving the brain and eyes) is recommended.
Is has a vascular malformation (port-wine stain or deeper) normal at 6-12 months?
For capillary malformations (port-wine stains), pulsed dye laser (PDL) treatment can begin in infancy and is more effective when started early. Multiple sessions are needed. The goal is to lighten the stain, though complete clearance is uncommon. For lymphatic malformations, treatment depends on size and location — options include sclerotherapy (injection treatment) and surgical reduction. Your vascular anomalies team will develop a plan tailored to your baby.
Should I go to the ER for has a vascular malformation (port-wine stain or deeper)?
Seek emergency care if a vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care, or if a lymphatic or venous malformation becomes suddenly swollen, red, and painful — this may indicate infection (cellulitis) and needs immediate medical treatment. When in doubt, call your pediatrician's after-hours line for guidance.
Does has a vascular malformation (port-wine stain or deeper) go away on its own?
In many cases, has a vascular malformation (port-wine stain or deeper) resolves on its own, especially when your baby has a port-wine stain that has been evaluated and you have a treatment plan with a vascular specialist. By 5 years+, long-term management of vascular malformations is a marathon, not a sprint. Most are managed rather than cured. Regular follow-up with a vascular anomalies team is important. New treatments continue to emerge, including targeted medications (such as sirolimus for complex lymphatic and venous malformations). Emotional support for children living with visible vascular malformations is an important part of care.

References

  1. [1]International Society for the Study of Vascular Anomalies. Classification of Vascular Anomalies. ISSVA
  2. [2]Boston Children's Hospital. Vascular Anomalies Center. Boston Children's
  3. [3]National Library of Medicine. Vascular Malformations. StatPearls, 2024. NIH

Doctor Visit Checklist

Bring this checklist to your next pediatrician visit to discuss My Baby Has a Vascular Malformation (Port-Wine Stain or Deeper).

Things to mention

  • Describe when you first noticed has a vascular malformation (port-wine stain or deeper) and how it has changed over time.
  • Note your baby's current age and which age-specific patterns you are seeing.
  • Mention if a port-wine stain on the face involves the forehead or eyelid area and has not been evaluated for Sturge-Weber syndrome.
  • Mention if a venous or lymphatic malformation seems to be growing disproportionately or causing pain.
  • Let your doctor know if you have noticed any related concerns, such as changes in feeding, sleep, or movement patterns.
  • Bring a list of any questions or observations you want to discuss at the appointment.

Observations to share

  • A port-wine stain on the face involves the forehead or eyelid area and has not been evaluated for Sturge-Weber syndrome
  • A venous or lymphatic malformation seems to be growing disproportionately or causing pain
  • The malformation is affecting function (vision, breathing, swallowing, limb movement)

Urgent signs to report immediately

  • A vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care
  • A lymphatic or venous malformation becomes suddenly swollen, red, and painful — this may indicate infection (cellulitis) and needs immediate medical treatment
  • Your baby has a facial port-wine stain and develops seizures — this could indicate Sturge-Weber syndrome and requires urgent neurologic evaluation

My notes

From ismybabyalright.com — free, evidence-based baby health guides

All content follows our editorial policy and is reviewed against published clinical guidelines.

2,705 evidence-based guides6 authoritative medical sources5 medical advisory board members

Bottom line

Most cases of has a vascular malformation (port-wine stain or deeper) are normal. Talk to your pediatrician if a vascular malformation is bleeding heavily and the bleeding does not stop with pressure — seek emergency care.

Trust your instincts. If something feels wrong, reach out to your pediatrician. Worrying about your baby means you care — that is a good thing.

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My Baby's Vascular Tumor Is Causing Blood Clotting Problems (Kasabach-Merritt)

Kasabach-Merritt phenomenon (KMP) is a rare but serious complication where certain vascular tumors (kaposiform hemangioendothelioma or tufted angioma — not common infantile hemangiomas) trap platelets and clotting factors, leading to dangerously low platelet counts and a bleeding disorder. KMP is a medical emergency that requires hospitalization and specialized treatment. Despite being frightening, modern treatment with sirolimus and other medications has significantly improved outcomes. Most children respond well to treatment, though the vascular tumor may not fully resolve.

My Baby Has a Waxy Yellowish Patch on Their Scalp (Nevus Sebaceous)

A nevus sebaceous (also called nevus sebaceous of Jadassohn) is a benign birthmark that typically appears on the scalp as a flat or slightly raised, yellowish-orange, waxy or velvety patch where hair does not grow. It is present at birth and occurs in about 0.3% of newborns. During childhood, it remains relatively flat and inconspicuous. At puberty, it becomes thicker and more noticeable due to hormonal stimulation. There is a small risk (historically overstated) of developing benign or rarely malignant tumors within the nevus later in life, so monitoring and potential removal are discussed with your dermatologist.

My Baby Has a Streaky or Velvety Raised Birthmark (Epidermal Nevus)

An epidermal nevus is a benign (non-cancerous) overgrowth of skin cells that is present at birth or appears in early childhood. It typically looks like a slightly raised, skin-colored to brownish, velvety or wart-like patch that often follows a linear or streaky pattern along the body's natural skin lines (Blaschko lines). Epidermal nevi are usually isolated and purely cosmetic. However, when they are large or extensive, they can sometimes be associated with abnormalities in other organ systems (epidermal nevus syndrome), so a thorough evaluation is recommended for larger lesions.

My Baby Has an Extra Nipple (Accessory Nipple)

Accessory (supernumerary) nipples are one of the most common minor congenital findings, occurring in about 1 in 18 people. They appear as small, flat, often pigmented bumps along the "milk line" — an embryonic line running from the armpit to the groin on each side. Most people mistake them for moles. Accessory nipples are almost always harmless and require no treatment. In rare cases, they may be associated with kidney abnormalities, so some pediatricians recommend a renal ultrasound if one is found, though this practice varies.

My Baby Was Born with a Raw Spot on Their Scalp (Aplasia Cutis)

Aplasia cutis congenita (ACC) is a condition where a baby is born with a small area of missing skin, most commonly on the scalp. It occurs in about 1 in 10,000 births. The affected area may look like a raw wound, an ulcer, or may have already healed into a thin, shiny scar by the time of birth. Most cases are small, isolated, and heal well with basic wound care — the area eventually forms a hairless scar. Larger defects or those associated with other findings may need more investigation, but isolated small ACC has an excellent prognosis.

New Treatments for Atopic Dermatitis (Eczema) in Children

Treatment for atopic dermatitis in children has advanced significantly in recent years. While moisturizers and topical steroids remain first-line treatments, newer options include non-steroidal topical medications (like crisaborole), biologic therapies (like dupilumab, approved for children 6 months and older), and JAK inhibitors. Most children's eczema is well-managed with basic skin care and mild topical treatments, but these newer options provide hope for moderate-to-severe cases.